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Complete Health Indicator Report of Birth Defects: Prevalence of Hypoplastic Left Heart Syndrome per 10,000 Live Births

Definition

Hypoplastic left heart syndrome (HLHS) is a problem with the heart's structure that is present at birth (congenital). It is a group of related defects that, together, mean that the left side of the heart is underdeveloped. The prevalence of HLHS is the number of live-born infants with HLHS per 10,000 live born infants. (Live-born infants are the infants born with any evidence of life).

Numerator

Number of live-born infants with hypoplastic left heart syndrome (HLHS).

Denominator

Number of live-born infants.

Data Interpretation Issues

In January 2000, birth defects became a reportable condition in New Mexico; however, birth defects were collected prior to this date. The first year of consistent data is 1998. However, data for hypoplastic left heart syndrome were not collected consistently until 2004. The most recent year of analyzed data is 2011.

Data are collected on live births occurring in-state to NM residents. Therefore, live births that occur in NM among out-of-state residents are excluded.

Case finding/identification occurs through review of birth and death certificates, hospital discharge diagnoses, records from pediatric specialists and prenatal diagnostic providers.

Birth defect cases are ascertained up to age 4; however, the majority of diagnoses are made by age 1.

Why Is This Important?

Birth defects pose a significant public health problem. One in 33 babies is born with a structural birth defect in the United States. Birth defects are a leading cause of infant mortality and responsible for considerable morbidity and disability.

Among people with HLHS, the underdeveloped left side of the heart is unable to provide enough blood flow to the body. The normal shunts present at birth help to direct blood to the body; when these connections close the oxygen-rich blood supply decreases. Thus, babies with HLHS might look normal at birth, but will develop symptoms of HLHS within a few days. These symptoms might include:
-Poor feeding
-Problems breathing
-Pounding heart
-Weak pulse
-Ashen or bluish skin color

Without treatment, babies with HLHS die. Although this defect cannot be corrected, surgeries after birth can create the needed connections, or shunts, to allow the blood to get to the body.

Other Objectives

CDC Environmental Public Health Tracking, Nationally Consistent Data and Measures (EPHT NCDM)

How Do We Compare With the U.S.?

The national prevalence of hypoplastic left heart among births from 2004-2006 is 2.3 per 10,000 births. These data data come from 14 birth defects surveillance programs: Arkansas, Arizona, California [8-county Central Valley], Colorado, Georgia [5-county metropolitan Atlanta], Illinois, Iowa, Kentucky, Massachusetts, North Carolina, Oklahoma, Puerto Rico, Texas, and Utah. Fore more information, please see: http://www.cdc.gov/ncbddd/features/birthdefects-keyfindings.html

Due to variability in the methods used by state birth defects surveillance systems and differences in populations and risk factors, state prevalence estimates may not be directly comparable with national estimates or those of other states.


Graphical Data Views

Hypoplastic Left Heart Syndrome - Five Year Average Prevalence per 10,000 Live Births 2006-2011

::chart - missing::

NM vs. U.S. Year Prevalence per 10,000 Live Births Lower Limit Upper Limit
Record Count: 2
New Mexico 2006-2010 1.1 0.5 1.6
New Mexico 2007-2011 1.3 0.7 1.9

Data Notes

New Mexico live-born infants with hypoplastic left heart syndrome (HLHS), 2006-2011.

The following International Classification of Diseases, 9th Revision, Clinical Modification (ICD-9-CM) codes were used to identify HLHS: 746.7.

In 1987, CDC put forth a set of 6 digit codes (the sixth digit provides greater specificity for diagnosis) based on the British Pediatric Association Classification of Diseases and the ICD-9-CM. If CDC/BPA codes are present, the following were used to identify HLHS: 746.700.


Prevalence of Hypoplastic Left Heart Syndrome by County 2006-2011

::chart - missing::
confidence limits

County Prevalence per 10,000 Live Births Lower Limit Upper Limit Note Numer- ator Denom- inator
Record Count: 35
Bernalillo 1.5 0.4 2.5 Rate is statistically unstable. 8 54,812
Catron 0 0 0 Rate is statistically unstable. 0 117
Chaves 1.6 0 4.9 Rate is statistically unstable. 1 6,092
Cibola 0 0 0 Rate is statistically unstable. 0 2,551
Colfax 0 0 0 Rate is statistically unstable. 0 832
Curry 0 0 0 Rate is statistically unstable. 0 4,978
De Baca 0 0 0 Rate is statistically unstable. 0 131
Dona Ana 0 0 0 Rate is statistically unstable. 0 15,759
Eddy 0 0 0 Rate is statistically unstable. 0 4,519
Grant 4.6 0 13.7 Rate is statistically unstable. 1 2,165
Guadalupe 0 0 0 Rate is statistically unstable. 0 260
Harding 0 0 0 Rate is statistically unstable. 0 27
Hidalgo 0 0 0 Rate is statistically unstable. 0 355
Lea 0 0 0 Rate is statistically unstable. 0 6,428
Lincoln 0 0 0 Rate is statistically unstable. 0 1,281
Los Alamos 0 0 0 Rate is statistically unstable. 0 1,041
Luna 0 0 0 Rate is statistically unstable. 0 2,319
McKinley 2.6 0 6.2 Rate is statistically unstable. 2 7,637
Mora 0 0 0 Rate is statistically unstable. 0 266
Otero 2 0 5.8 Rate is statistically unstable. 1 5,129
Quay 0 0 0 Rate is statistically unstable. 0 610
Rio Arriba 2.6 0 7.8 Rate is statistically unstable. 1 3,806
Roosevelt 0 0 0 Rate is statistically unstable. 0 1,748
Sandoval 1.1 0 3.2 Rate is statistically unstable. 1 9,366
San Juan 0.9 0 2.6 Rate is statistically unstable. 1 11,435
San Miguel 0 0 0 Rate is statistically unstable. 0 2,095
Santa Fe 2.1 0 5 Rate is statistically unstable. 2 9,552
Sierra 0 0 0 Rate is statistically unstable. 0 591
Socorro 0 0 0 Rate is statistically unstable. 0 1,512
Taos 0 0 0 Rate is statistically unstable. 0 2,110
Torrance 0 0 0 Rate is statistically unstable. 0 1,060
Union 0 0 0 Rate is statistically unstable. 0 181
Valencia 3.4 0 8.1 2 5,871
Missing/unknown 0 0 0 Rate is statistically unstable. 0 2
NM 1.2 0.7 1.7 20 166,638

Data Notes

New Mexico live-born infants with hypoplastic left heart syndrome (HLHS), 2006-2011.

The following International Classification of Diseases, 9th Revision, Clinical Modification (ICD-9-CM) codes were used to identify HLHS: 746.7.

In 1987, CDC put forth a set of 6 digit codes (the sixth digit provides greater specificity for diagnosis) based on the British Pediatric Association Classification of Diseases and the ICD-9-CM. If CDC/BPA codes are present, the following were used to identify HLHS: 746.700.

Data Sources

  • Birth Defects Prevention and Surveillance System (BDPASS), New Mexico Department of Health.
  • Birth Certificate Data, Bureau of Vital Records and Health Statistics (BVRHS), New Mexico Department of Health.


Hypoplastic Left Heart Syndrome: Four Year Counts - Five Year Average Prevalence per 10,000 Live Births 2006-2011

::chart - missing::

Year Case Counts
Record Count: 2
2006-2010 15
2007-2011 18

Data Notes

New Mexico live-born infants with hypoplastic left heart syndrome (HLHS), 2006-2011.

The following International Classification of Diseases, 9th Revision, Clinical Modification (ICD-9-CM) codes were used to identify HLHS: 746.7.

In 1987, CDC put forth a set of 6 digit codes (the sixth digit provides greater specificity for diagnosis) based on the British Pediatric Association Classification of Diseases and the ICD-9-CM. If CDC/BPA codes are present, the following were used to identify HLHS: 746.700.

More Resources and Links

Evidence-based community health improvement ideas and interventions may be found at the following sites:

Additional indicator data by state and county may be found on these Websites:

Medical literature can be queried at the PubMed website.

For an on-line medical dictionary, click on this Dictionary link.

Page Content Updated On 07/31/2014, Published on 07/31/2014
The information provided above is from the New Mexico Department of Health's NM-IBIS web site (http://ibis.health.state.nm.us). The information published on this website may be reproduced without permission. Please use the following citation: "Retrieved Wed, 01 April 2015 from New Mexico Department of Health, Indicator-Based Information System for Public Health Web site: http://ibis.health.state.nm.us".

Content updated: Tue, 12 Aug 2014 11:49:04 MDT